Case of the week 6 (
October 2011
) Congenital Esotropia in a bilateral Brown syndrome
child
The mother of this mentally retarded 5y old girl
complained that the left eye of her daughter
deviates inward since birth , no history of head trauma
, Examination revealed bilateral normal fundi ,
insignificant refractive error
First ,
I thought it is a straight forward case of infantile
Esotropia
But Motility examination completely disagreed
this initial wrong diagnosis
Watch video examination of this patient
First , you have to deal with what
bothers the parents i.e the esotropia - in many cases
like this I noticed that most parents are only aware of
the horizontal deviation , this is really right , since
the primary position is the most important cardinal
direction to be respected , so first to be done here is
BMR recession to correct the infantile esotropia
Then what
about the bilateral limitation of elevation of the
adducted eyes ?
This is a typical case of Bilateral
Brown syndrome. Of course, this must be confirmed by
demonstrating restricted forced ductions to elevation
in adduction
Second , You must think about the
differential diagnosis of this condition :
Strabismus Course : Lecture 17 :
Slide 51
You can simply exclude other causes
since there is no history of trauma ,
of course
this is not a thyroid eye disease , also there is
no history of previous strabismus or orbital surgeries ,
however IO palsy should be suspected since there is a
history of other neurological disorders together with
the facial asymmetry and the abnormal head circumference
See Forced duction Test in this patient
Based on the typical appearance, it
is safe to schedule surgery with confidence that the
diagnosis of Brown will be confirmed. The choice of
surgical procedure depends on the experience and the
preference of the surgeon.
1) The first surgical procedure is :
Expose the entire superior oblique tendon after a
‘cuffed’ superior limbal
incision, usually with detachment of the superior rectus
. explore the superior oblique tendon from the trochlear
cuff
to the tendon's insertion freeing any obvious
restrictions , replace the superior rectus and
close.
2) Still others would do a
superior oblique tenectomy.
3) For me I prefer a medial
approach to the superior oblique tendon and place a
silicone spacer to lengthen the tendon.
All of these procedures can succeed , sometimes all can
fail
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Strabismus & Oculomotor Disorders