The most striking features
in this infant are the left face turn and the limitation of abduction .
The clinician should be aware of other causes of
limitation of abduction in this age group ,
these are Duane Syndrome type I and III and Mobius syndrome
(Moebius syndrome is a bilateral congenital
paralysis of the abducens and facial nerves
resulting in esotropia and an expressionless
facial appearance. There is also atrophy of the
distal third of the tongue with a history of
poor feeding) , he should also be aware about
pseudo abducens palsy occuring in many infants
with congenital esotropia.
Infantile
esotropia and nystagmus blockage by
convergence are often accompanied by apparent
limitation of abduction. The doll's head
maneuver or patching of one eye distinguishes
pseudoabducens paralysis from a true paralysis
in these cases.
Congenital 6th
nerve palsy as an isolated phenomenon is
exceedingly rare but may occur from injury to
the abducens nerve shortly before or during
birth.
Congenital 6th
nerve palsy usually occurs with other neurologic
or systemic anomalies. Patients with cerebral
palsy seem to have an increased prevalence of
congenital 6th nerve palsy .
Surgical intervention
for congenital sixth nerve palsy is indicated
when the deviation has been stable for a minimum
of 10-12 months. The choice of surgical
procedure for sixth nerve palsies depends upon
the recovery of function of the lateral rectus
muscle, which can be assessed by determining the
saccadic velocity. Patients who have good return
of function usually do quite well with an
ipsilateral recess-resect procedure. Patients
who have little or no lateral rectus function
need muscle transposition surgery.