Home Page Strabismus Course Strabismus Books Strabismus Videos

Strabismus Lectures Case of the week E Consultation Contact me


Case of the week 86 ( November 2012 )
Congenital Esotropia


Congenital Esotropia

pre

post


Congenital, infantile, or essential infantile esotropia is the most common form of strabismus with onset during infancy for which no difficulty in diagnosis should be present.

Congenital (infantile) esotropia can be confirmed by the clinician at the age of 4 months . The required findings for diagnosis are:

1.    Esotropia which is usually of a large angle.

2.    Normal neurologic infant.

3.    Refractive error expected for age and correction of which does not eliminate esotropia.

Congenital esotropia is defined as an esotropia appears in the first 6 months of life in a neuorologically normal infants with bilateral normal eyes.

The infant with congenital ET has either alternation or fixation preference for one eye, implying amblyopia. Other findings may be present - but not needed for diagnosis - are: manifest nystagmus, latent nystagmus, oblique muscle dysfunction,DVD and face turn.

  Congenital esotropia is not the only ET with an onset during the first 6 months of life. There are other conditions, some are congenital which is present at birth, and others are acquired which appear during the first few months of life, like congenital esotropia.

Among the congenital conditions: congenital 6th nerve palsy, Duane syndrome type I, and Mobius syndrome.

Among the acquired conditions: sensory esotropia, refractive  esotropia, the nystagmus compensation (blockage) syndrome, or esotropia in association with other central nervous system manifestations, such as Down syndrome, albinism, cerebral palsy and mental retardation.

Although there is a huge debate about the origin and terminology of congenital esotropia, it is universally accepted by strabismologists that surgery is the treatment of choice for congenital ET after refractive ET is ruled out and after amblyopia (if present) is treated.

Infants with congenital ET should alternate fixation before surgery, however, amblyopia therapy can be continued after surgery.

The age chosen for surgery varies from one doctor to another, for me I prefer interference as early as the age of 4 months .

Surgery for infantile esotropia consists of bimedial rectus recession, medial rectus recession and lateral rectus resection of one eye, a three-muscle procedure combining a bimedial rectus recession with a resection of one lateral rectus or in a very few cases a four-muscle procedure consisting of a bilateral recession-resection.

Many cases of infantile esotropia who are operated at age less than 1 year may develop inferior oblique overaction months to years after initial horizontal muscle surgery in which case inferior oblique weakening is done as a second procedure.



الموقع المصري للحول وامراض الجهاز الحركي للعين

The Egyptian Site of Strabismus & Oculomotor Disorders